Case Report
Volume 11 Issue 9 - 2022
Intracranial Hemorrhage Associated with Biliary Atresia
Chafi S*
Pediatric Consultant, Pediatrics Service, Public Hospital of Bordj Bounaama Tissemsilt, Algeria
*Corresponding Author: Chafi S, Pediatrics Consultant, Pediatrics Service, Public Hospital of Bordj Bounaama Tissemsilt, Algeria.
Received: July 18, 2022; Published: August 30, 2022


Biliary atresia (BA) is a rare disease characterized by biliary obstruction in which the etiology remains obscure. In this report we describe a case of 40 days old female child fully breastfed that had not received vitamin K prophylaxis after birth. The latter presented to paediatric emergency department with severe jaundice, abnormal neurological exam and hepatomegaly, head CT scan was suggestive of massive left temporal intra parenchymatous and sub-Arachnoid hemorrhage related to vitamin k deficiency, neonatal cholestasis has been found to be related to biliary atresia which has led to vitamin k deficiency. After the enfant has recovered neurologically he has been referred to paediatric surgery team where a Kasai Portoenterostomy procedure has been done timely. Thus biliary atresia should be considered in all patients with cholestasis because early diagnosis could prevent severe complications and results in a better prognosis.

Keywords: Biliary Atresia; Intracranial Hemorrhage; Vitamin K Deficiency; Kasai Portoenterostomy; Neonatal Cholestasis


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Citation: Chafi S. “Intracranial Hemorrhage Associated with Biliary Atresia”. EC Paediatrics 11.9 (2022): 82-86.

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