Case series
Volume 19 Issue 8 - 2020
Ectodermal Dysplasia: Diagnosis and Dental treatment
Anup Cholepatil1*, Nikita Kale2, Aniruddha Deshpande1 and Kapil Pawar3
1Department of Periodontology, CSMSS Dental College, Aurangabad, India
2Department of Prosthodontics, CSMSS Dental College, Aurangabad, India
3Department of Oral diagnosis and Radiology, CSMSS Dental College, Aurangabad, India
*Corresponding Author: Anup Cholepatil, Associate Professor, Department of Periodontology, CSMSS Dental College, Aurangabad, India.
Received: July 17, 2020; Published: July 29, 2020


Ectodermal dysplasia is characterized by the absence of or defect of 2 or more ectodermally derived structures. It is characterized by the triad of signs comprising sparse hair (hypotrichosis), abnormal or missing teeth (anodontia or hypodontia) and inability to sweat due to lack of sweat glands. Most patients with ED have a normal life expectancy and normal intelligence. However, the lack of sweat glands may lead to hyperthermia, followed by brain damage or death in early infancy, if unrecognized. Thus, an early diagnosis is important. This article consists of 2 case repots of ectodermal dysplasia. Common dental, oral and physical conditions were taken into account. Clinical management includes removable or fixed partial denture to promote better functioning of stomatognathic system.

Keywords: Anodontia; Ectodermal Dysplasia; Hypodontia; Hypotrichosis


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Citation: Anup Cholepatil., et al. “Ectodermal Dysplasia: Diagnosis and Dental treatment”. EC Dental Science 19.8 (2020): 158-166.

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