Abstract

Ectodermal dysplasia is characterized by the absence of or defect of 2 or more ectodermally derived structures. It is characterized by the triad of signs comprising sparse hair (hypotrichosis), abnormal or missing teeth (anodontia or hypodontia) and inability to sweat due to lack of sweat glands. Most patients with ED have a normal life expectancy and normal intelligence. However, the lack of sweat glands may lead to hyperthermia, followed by brain damage or death in early infancy, if unrecognized. Thus, an early diagnosis is important. This article consists of 2 case repots of ectodermal dysplasia. Common dental, oral and physical conditions were taken into account. Clinical management includes removable or fixed partial denture to promote better functioning of stomatognathic system.

Keywords: Anodontia; Ectodermal Dysplasia; Hypodontia; Hypotrichosis

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