Case Report
Volume 7 Issue 2 - 2020
A Rare Association: Lutembacher Syndrome and Coarctation of Aorta
Saousan Serbout1*, Fatima Ezzahra Talhi1, Ayoub Abetti2, O Elallam3, S Lyazidi2, L Azzouzi1, A Drighil1, R Habbal1, C El Kettani3, EH Barrou3 and Youssef Ettaoumi2
1Department of Cardiology, Ibn Rushd Hospital University, Casablanca, Morocco
2Department of Cardiovascular Surgery, Ibn Rushd Hospital University, Casablanca, Morocco
3Department of Anesthesiology and Reanimation, Casablanca, Morocco
*Corresponding Author: Saousan Serbout, Department of Cardiology, Ibn Rushd Hospital University, Casablanca, Morocco.
Received: December 13, 2019; Published: January 21, 2020


Lutembacher syndrome is defined by a congenital ostium secundum atrial septal defect associated to an acquired mitral valve stenosis. We present a similar case in a 24 year old female who came in with progressive shortness of breath. Examination revealed an elevated jugular vein distention. The first heart sound is loud in all four cardiac areas, a wide fixed split of second heart sound on inspiration and expiration and a grade 2/6 systolic murmur at of tricuspid regurgitation. Chest x-ray showed signs of pulmonary edema with bat wing pattern and cardiomegaly. Electrocardiography (ECG) revealed an electrical axis shifted to the right and right bundle branch block along and Transthoracic Echocardiography (TTE) showed a mitral stenosis with calcification and moderate tricuspid regurgitation, dilated cardiac chambers and coarctation of aorta. The patient was consequently treated with symptomatic drugs contain beta-blockers and diuretics and finally a scheduled for valvular and septal repair via open heart surgery. The purpose of this case report is to assist cardiologists in diagnosing this syndrome accurately on the basis of symptoms and investigations.

Keywords: Atrial Septal Defect; Lutembacher Syndrome; Mitral Stenosis; Transthoracic Echocardiography


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Citation: Saousan Serbout., et al. “A Rare Association: Lutembacher Syndrome and Coarctation of Aorta”. EC Cardiology 7.2 (2020): 01-07.

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