Case Report
Volume 9 Issue 3 - 2022
Scimitar Syndrome with Tetralogy of Fallot: A Very Rare Association
Hanane Mechal* and Abdenasser Drighil
Cardiology Department, University Hospital Center of Casablanca, Morocco
*Corresponding Author: Hanane Mechal, Cardiology Department, University Hospital Center of Casablanca, Morocco.
Received: April 22, 2022; Published: April 29, 2022


Scimitar syndrome is a rare variant of partial anomalous pulmonary venous connection. The association of Scimitar syndrome with another cardiac congenital anomaly such as tetralogy of Fallot is very rare; It may proceed unnoticed, as cyanosis already predominates in the clinical picture. Data about optimal therapeutic strategy in this rare variant of SS are scarce. We are reporting the case of an eighteen-month old boy diagnosed with Scimitar syndrome and tetralogy of Fallot treated with pneumonectomy.

Keywords: Scimitar Syndrome; Scimitar Vein; Tetralogy of Fallot; Anomalous Pulmonary Venous Drainage


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Citation: Hanane Mechal and Abdenasser Drighil. “Scimitar Syndrome with Tetralogy of Fallot: A Very Rare Association”. EC Cardiology 9.3 (2022): 40-47.

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