Case Report
Volume 9 Issue 3 - 2022
Scimitar Syndrome with Tetralogy of Fallot: A Very Rare Association
Hanane Mechal* and Abdenasser Drighil
Cardiology Department, University Hospital Center of Casablanca, Morocco
*Corresponding Author: Hanane Mechal, Cardiology Department, University Hospital Center of Casablanca, Morocco.
Received: April 22, 2022; Published: April 29, 2022




Abstract

Scimitar syndrome is a rare variant of partial anomalous pulmonary venous connection. The association of Scimitar syndrome with another cardiac congenital anomaly such as tetralogy of Fallot is very rare; It may proceed unnoticed, as cyanosis already predominates in the clinical picture. Data about optimal therapeutic strategy in this rare variant of SS are scarce. We are reporting the case of an eighteen-month old boy diagnosed with Scimitar syndrome and tetralogy of Fallot treated with pneumonectomy.

Keywords: Scimitar Syndrome; Scimitar Vein; Tetralogy of Fallot; Anomalous Pulmonary Venous Drainage

References

  1. Cruz-Martínez R and Gratacós E. “5 - Scimitar Syndrome”. In: Copel JA, D’Alton ME, Feltovich H, Gratacós E, Krakow D, Odibo AO, et al., editors. Obstetric Imaging: Fetal Diagnosis and Care (Second Edition) (2018): 22-25.
  2. Biyyam DR., et al. “Congenital lung abnormalities: embryologic features, prenatal diagnosis, and postnatal radiologic-pathologic correlation”. Radiogr Rev Publ Radiology Soc N American Inc 30.6 (2010): 1721-1738.
  3. Chakraborty RK., et al. “Pulmonary Sequestration”. In: StatPearls. Treasure Island (FL): StatPearls Publishing (2021).
  4. Çınar B., et al. “A Rare Associated Anomaly in Tetralogy of Fallot: Scimitar Syndrome in an Infant”. Brazilian Journal of Cardiovascular Surgery4 (2021): 578-580.
  5. Ismail SR., et al. “Scimitar syndrome with tetralogy of fallot and pulmonary atresia”. The Egyptian Heart Journal 67.3 (2015): 275-277.
  6. Sun J hong., et al. “Scimitar syndrome with the left persistent superior vena cava”. Surgical and Radiologic Anatomy (2008).
  7. Castaldi B and Milanesi O. “Chapter 7 - Natural History and Medical Treatment”. In: Vida VL, editor. The Complete Reference for Scimitar Syndrome. Academic Press (2017): 91-103.
  8. Redington AN., et al. “Tetralogy of Fallot with anomalous pulmonary venous connections: a rare but clinically important association”. British Heart Journal5 (1990): 325-328.
  9. Talwar S., et al. “Tetralogy of Fallot with anomalous systemic and pulmonary venous drainage, anomalous coronary artery pattern, and abnormal development of diaphragm”. Congenital Heart Disease1 (2009): 21-24.
  10. Çınar B., et al. “A Rare Associated Anomaly in Tetralogy of Fallot: Scimitar Syndrome in an Infant”. Brazilian Journal of Cardiovascular Surgery4 (2021): 578-580.
  11. Katekaru-Tokeshi DI., et al. “Tetralogy of Fallot with Scimitar Syndrome”. Radiology: Cardiothoracic Imaging - RSNA Journals5 (2020): e200253.
  12. Mulligan ME. “History of scimitar syndrome”. Radiology1 (1999): 288-290.
  13. Gutierrez J., et al. “Tetralogía de Fallot asociada a síndrome de cimitarra”. Revista Colombiana de Cardiología (2012).
  14. Mordue BC. “A case series of five infants with scimitar syndrome”. Advances in Neonatal Care3 (2003): 121-132.
  15. Espinola-Zavaleta N., et al. “Clinical and Echocardiographic Characteristics of Scimitar Syndrome”. Revista Española de Cardiología3(2006): 284-288.
  16. Keller RL., et al. “Chapter 49 - Surgical Disorders of the Chest and Airways”. In: Gleason Christine A, Devaskar SU, editors. Avery’s Diseases of the Newborn (Ninth Edition). Philadelpia: W.B. Saunders (2012): 672-697.
  17. Najm HK., et al. “Scimitar syndrome: twenty years’ experience and results of repair”. The Journal of Thoracic and Cardiovascular Surgery5 (1996): 1161-1168.
  18. Uthaman B., et al. “The impact of interruption of anomalous systemic arterial supply on scimitar syndrome presenting during infancy”. Catheterization and Cardiovascular Interventions5 (2008): 671-678.
  19. Vida VL., et al. “Scimitar Syndrome”. Circulation12 (2010): 1159-1166.
  20. Alsoufi B., et al. “Outcomes after surgical treatment of children with partial anomalous pulmonary venous connection”. The Annals of Thoracic Surgery6 (2007): 2020-2026.
  21. Dupuis C., et al. “Infantile’ form of the scimitar syndrome with pulmonary hypertension”. The American Journal of Cardiology15 (1993): 1326-1330.
  22. Vida VL and Guariento A. “A sword threatening the heart: The scimitar syndrome”. JTCVS Techniques 1 (2020): 75-80.
  23. Sfyridis PG., et al. “Emergency Transmediastinal Pneumonectomy for Scimitar Syndrome”. World Journal for Pediatric and Congenital Heart Surgery3 (2010): 389-392.
  24. Kamiyama M., et al. “Scimitar syndrome treated with pneumonectomy: a case associated with bronchospastic attack”. Pediatric Surgery International1 (2004): 65-66.
  25. Huddleston CB., et al. “Scimitar syndrome presenting in infancy”. The Annals of Thoracic Surgery1 (1999): 154-159.
  26. Laros CD and Westermann CJ. “Dilatation, compensatory growth, or both after pneumonectomy during childhood and adolescence. A thirty-year follow-up study”. The Journal of Thoracic and Cardiovascular Surgery4 (1987): 570-576.
  27. Azhari N., et al. “Tetralogy of Fallot associated with scimitar syndrome”. Cardiology in the Young1 (2000): 70-72.
Citation: Hanane Mechal and Abdenasser Drighil. “Scimitar Syndrome with Tetralogy of Fallot: A Very Rare Association”. EC Cardiology 9.3 (2022): 40-47.

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