Case Series
Volume 7 Issue 8 - 2020
Echocardiographic Findings in Congenital Mitral Ring: A Report of Three Cases
Hakim Kaouthar*, Ben Othmen Rihab, Hentati Mouna, Msaad Hela and Ouarda Fatma
Pediatric Cardiology Department, La Rabta Hospital, Faculty of Medecine, Tunis Manar University, Tunisia
*Corresponding Author: Hakim Kaouthar, Pediatric Cardiology Department, La Rabta Hospital, Faculty of Medecine, Tunis Manar University, Tunisia.
Received: June 03, 2020; Published: July 29, 2020


Mitral ring, also known as membranous supravalvular mitral stenosis is a rare congenital heart defect of surgical importance. It may be encountered in isolation or more often in association with other cardiac anomalies. Transthoracic echocardiography is the gold standard to define the anatomy of the ring and mitral valve, to assess the severity of obstruction, and to identify any associated defect. The purpose of this article is to present 3 pediatric cases with Supramitral ring (SMR) and to focus on the value of transthoracic echocardiography in diagnosis and evaluation of this cardiac anomaly and eventual associated lesions. Recognition is important because surgical results are better than for other forms of congenital mitral stenosis.

Keywords: Congenital Mitral Stenosis; Supramitral Ring; Transthoracic Echocardiography


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Citation: Hakim Kaouthar., et al. “Echocardiographic Findings in Congenital Mitral Ring: A Report of Three Cases”. EC Cardiology 7.8 (2020): 54-59.

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