Case Report
Volume 4 Issue 3 - 2021
Botryoid Rhabdomyosarcoma of Nasopharynx: Case Report and Litterature Review
Merzouqi B1*, Salama K1, Lahjaouj M1, Rouadi S2, Abada R2, Roubal M2 and Mahtar M2
1Department of ENT, 20 August Hospital, Ibn Rochd University Hospital, Casablanca, Moroc
2Department of ENT, 20 August Hospital, Ibn Rochd University Hospital, Faculty of Medicine and Pharmacy, Casablanca, Morocco
*Corresponding Author: Merzouqi Boutaina, Department of ENT, 20 August Hospital, Ibn Rochd University Hospital, Casablanca, Morocco.
Received: January 02, 2021; Published: February 25, 2021




Abstract

Rhabdomyosarcoma (RMS) is a rare and aggressive malignancy originating from primitive mesenchymal cells that arise anywhere in the body, including sites where striate muscle is not found or scanty. RaMS is the most common type of soft-tissue sarcoma in young children, representing 5% of all childhood malignancies. Almost half of RMS occur in the head and neck with three different primary sites being recognized: parameningeal (PM), non-PM (NPM) and orbital (ORB). RMS of the nasopharynx represents an invasive and destructive form of the skull base. The prognosis of infiltrative form is reserved compared to that of localized forms. Treatment is mainly based on chemotherapy, radiotherapy or surgery depending on the location. We report a case of a 7yr-old child with a huge facial mass invading the skull base with a massive extension via the nasopharynx complicated by a right Orbital Apex Syndrome, the diagnosis of botryoid RMS was made and a multiple courses of chemoradiotherapy was performed with a slight improvement.

Keywords: Rhabdomyosarcoma; Nasopharynx; Mesenchymal Cells; Children

References

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Citation: Merzouqi Boutaina.,et al. “Botryoid Rhabdomyosarcoma of Nasopharynx: Case Report and Litterature Review”. EC Clinical and Medical Case Reports 4.3 (2021): 31-36.

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