Case Report
Volume 3 Issue 8 - 2020
Case Report: Obstructed Hemivagina and Ipsilateral Renal Anomaly (OHVIRA) Syndrome
Maria Jabeen and Haleema A Hashmi*
Obstetrics and Gynaecology, Liaquat National Hospital, Karachi, Pakistan
*Corresponding Author: Haleema A Hashmi, Professor of Obstetrics and Gynaecology, Liaquat National Hospital, Karachi, Pakistan.
Received: June 16, 2020; Published: July 29, 2020




Abstract

OHVIRA syndrome is a rare variety type III mullerian duct congenital anomaly. The syndrome includes uterine didelphys, obstructed hemivagina and ipsilateral renal anatomy, also known as Herlyn-Werner Wunderlich (HWW) syndrome. It is characterized by congenital birth defect of the lower abdominal organs and pelvic organs.

Mullerian malformation results from defective fusion of the mullerian duct during development of the female reproductive system. American fertility society classification of mullerian anomalies is the most commonly used standard classification.

 We report a case of 14 year old young girl presented in outpatient clinic with complain of irregular vaginal bleeding associated with abdomino pelvic pain for 4 months. She had menarche 4 months back. The history was suggestive of developmental anomaly of vagina. Trans abdominal ultrasound done, followed by magnetic resonance imaging (MRI) of pelvis with contrast MRI is most sensitive diagnostic modality for pelvic abnormalities. After confirmation of the diagnosis surgical intervention was suggested, initially parents refused but later agreed. Surgical correction done successfully with drainage of menstrual blood and partial resection of the vaginal septum. Detailed informed consent was recorded in file.

 Key Words: Obstructed Hemivagina and Ipsilateral Renal Anomaly (OHVIRA); Herlyn-Werner Wunderlich (HWW) syndrome; Transvaginal Septuml Renal Agenesis; Laparoscopy and Hysteroscopy

References

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Citation: Maria Jabeen and Haleema A Hashmi. “Case Report: Obstructed Hemivagina and Ipsilateral Renal Anomaly (OHVIRA) Syndrome”. EC Clinical and Experimental Anatomy 3.8 (2020): 14-18.

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